- Systemic including: Skin, kidneys, respiratory tract (upper and lower), brain, blood vessels of all sizes, nerves, GI tract
- Idiopathic (cutaneous only) vasculitis (39%)
- Primary systemic vasculitis (14%): Henosch-Schonlein Purpura (HSP), Granulomatosis w/Polyangiitis (GPA), Polyarteriitis Nodosa (PAN), Eosoinophilic Granulomatosis w/Polyangiitis (EGPA), Microscopic Poyangiitis (MPA), Giant Cell Arteriitis (GCA)
- Connective tissue disease (11%): Lupus, Rheumatoid Arthritis, Sjogren's
- Other systemic disorders (2%): Behcet's, Sarcoidosis, IBD, Cryoglobulinemia
- Infections (22%): upper respiratory tract, viral hepatitis, Strep, Staph or other systemic bacteremias
- Variable, depending on type of vasculitis and organ system(s) affected
- Can include generalized (fever, chills, sweats, weight loss) or organ specific (cough, hemoptysis, finger pain/ulcers, hematuria, etc)
- Purpura (typically palpable)
- Pain, swelling, distal ischemia/necrosis (in particular nose, fingers, toes)
- Other findings based on organ system affected (e.g. nasal septal ulcer/perforation w/GPA)