Right Ventricular Dysplasia (Arrhythmogenic RV Dysplasia)

Etiology

  • Idiopathic right ventricular structural abnormalities (RV muscle replaced by fat, fibrotic tissue)

Risk Factors

  • Presentation < 40yo, though can be any age
  • Sometimes precipitated by exercise, athletic competition
  • May have family history

Symptoms

  • Presyncope, syncope, sudden death
  • Palpitations, SOB, awareness of racing heart

Tests