Lymphangioleiomyomatosis (LAM)

Etiology

  • Rare
  • Cystic lung dz of unknown etiology

Risk Factors

  • W>m
  • Hx tuberous sclerosis

Symptoms

  • Doe
  • Cough
  • Sub-acute, progressive sob from decline in FEV1 related to cysts
  • Can present with recurrent pneumothorax
  • Other associated disorders: Chylous pleural effusion from lymphatic obstruction; Renal angiomyolipomas; Retroperitoneal LAM

Tests