- Affects greater area of skin than lcSSc
- Proximal and distal
- More rapidly progressive,
- Tightening/thickened fingers
- Telangiectasias, raynauds→ finger hypoperfusion and pain in cold
- Sub-cu nodules less common
- GERD, which can lead to Barretts (and then cancer), scarring; also dysphagia
- Internal organs involvement includes: sob from interstitial lung dz, but plum htn less common
- Athralgias & myalgias
- Scleroderma renal crisis; pericarditis
- Raynauds → fingers blanch/hurt when exposed to cold temp
- Skin thickening/tightness
- Dry crackles if interstitial lung disease