Pulmonary AVM (HHT, Hepato-Pulm)

Etiology

  • Most commonly assoc w/hereditary hemorrhagic telangiectasia (HHT; formerly Osler-Weber-Rendu) within lungs
  • Also congenital, assoc w/cirrhosis→ hepato-pulm syndrome
  • Or w/prior surgery/trauma

Symptoms

  • Sob
  • Doe

Physical Exam Findings

  • Findings associated w/advanced liver dz if related to cirrhosis (i.e. jaundice, icterus, ascites, edema, gynecomastia, muscle wasting)
  • Telangiectasis on nasal mucosa, lips, tongue and GI tract can cause bleeding in those areas

Links