- Unusual neuroendocrine tumor based in pancreas
- Associated w/MEN1 (rare): hyper-parathyroidism, pancreas (gastrin, VIP, insulin) and pituitary (GH, Prolactin) producing tumors
- And pain related to associated ulcers
- Heartburn/GERD sx
- Secretory watery diarrhea→ persists w/fasing, nocturnal symptoms, cramps
- Elevated serum gastrin level