Pulmonary Hypertension

Group 1: idiopathic, HIV, drug induced (meds for weight loss), connective tissue disease, portal hypertension, congenital heart dz, schistosomiasis Group 2: Related to left heart failure (HFpEF, HFrEF), valvular heart disease Group 3: Related to copd, restrictive lung dz, ILD, OSA, hypoxia without lung dz Group 4: Related to chronic thrombo-embolic disease Group 5: Unclear etiology, multifactorial, other: e.g. sarcoid, hematologic (e.g. p vera, essential thrombocytosis), other

Your Path

  • Pulmonary Hypertension


  • Can include: SOB, DOE, chest pain, syncope, other related to underlying process/associated disorder

Physical Exam Findings

  • Findings related to underlying disorders (if present)
  • Sometimes low O2 sat, abnormal VS (if uncompensated)
  • Elevated JVP, edema, murmur TR